TY - JOUR
T1 - Case Series of Berry syndrome
T2 - A rare constellation of fatal cardiac anomalies
AU - Tandayu, Kevin Moses Hanky
AU - Kurniawati, Yovi
AU - Atmosudigdo, Indriwanto Sakidjan
AU - Lilyasari, Oktavia
N1 - Publisher Copyright:
© 2024 Annals of Pediatric Cardiology.
PY - 2023
Y1 - 2023
N2 - Berry syndrome is an extremely rare constellation of several congenital cardiac anomalies consisting of aortopulmonary window, aortic origin of the right pulmonary artery (AORPA), interrupted aortic arch or hypoplastic aortic arch or coarctation of the aorta, and an intact ventricular septum with high neonatal mortality rates. The disease is fatal with high mortality (90%) in the neonatal period with surviving patients mostly developing pulmonary hypertension. We describe the clinical presentation and diagnostic clues in two patients with Berry syndrome.
AB - Berry syndrome is an extremely rare constellation of several congenital cardiac anomalies consisting of aortopulmonary window, aortic origin of the right pulmonary artery (AORPA), interrupted aortic arch or hypoplastic aortic arch or coarctation of the aorta, and an intact ventricular septum with high neonatal mortality rates. The disease is fatal with high mortality (90%) in the neonatal period with surviving patients mostly developing pulmonary hypertension. We describe the clinical presentation and diagnostic clues in two patients with Berry syndrome.
KW - Aortic origin of the right pulmonary artery
KW - aortopulmonary window
KW - Berry syndrome
KW - congenital heart disease
KW - interrupted aortic arch
UR - http://www.scopus.com/inward/record.url?scp=85189544019&partnerID=8YFLogxK
U2 - 10.4103/apc.apc_109_23
DO - 10.4103/apc.apc_109_23
M3 - Article
AN - SCOPUS:85189544019
SN - 0974-2069
VL - 16
SP - 374
EP - 377
JO - Annals of Pediatric Cardiology
JF - Annals of Pediatric Cardiology
IS - 5
ER -
