A rare case of multiple leiomyomas on rudimentary uterus in a woman with Mayer Rokitansky Kuster Hauser (MRKH) syndrome: A challenging diagnosis and laparoscopic approach

Achmad Kemal Harzif, Sonia Ambalagen, Fistyanisa Elya Charilda, Heidi Dewi Mutia

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1 Citation (Scopus)

Abstract

Mayer Rokitansky Kuster Hauser (MRKH) syndrome is a congenital disorder involving reproductive, genitourinary, bone, and cardiac malformation. The incidence is 1 in 4000–5000 females livebirths. The phenotype is female 46 XX karyotype, normal secondary sexual characteristics, and normal functional ovaries. The occurrence of leiomyoma in uterine remnant in MRKH syndrome is a very rare case, even though several cases have been reported. The diagnosis and management approach, in this case, is quite challenging. Here, we report a 38 years old female who represents multiple leiomyomas on the rudimentary uterus, then we did laparoscopic removal of the fibroids and adjacent rudimentary uterus.

Original languageEnglish
Article number105711
JournalInternational Journal of Surgery Case Reports
Volume81
DOIs
Publication statusPublished - Apr 2021

Keywords

  • Case report
  • Laparascopic
  • Mayer Rokitansky Kuster Hauser (MRKH) syndrome
  • Multiple leiomyomas
  • Rudimentary uterus

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